XML Linking Language , or XLink , is an XML markup language and W3C specification that provides methods ... links. ref citation url http www.w3.org TR NOTE xlink req title XML XLink Requirements publisher W3C date 1999 02 24 last DeRose first Steven J. ref The XLink specification XLink 1.1 is a W3C recommendation ... TR xlink11 publisher W3C title XML Linking Language XLink Version 1.1 date May 6, 2010 ref and the successor of XLink 1.0, which was also a W3C recommendation. ref name xlink10 citation url http www.w3.org TR xlink publisher W3C title XML Linking Language XLink Version 1.0 date June 8, 2006 ref Linking with XLinkXLink defines a set of Attribute computing XML attributes that may be added to elements of other XML namespaces . XLink provides two kinds of hyperlinking for use in XML documents. Simple ... xmlns http example.org xmlns 2002 document xmlns xlink http www.w3.org 1999 xlink heading id someHeading Some Document heading para Here is anchor xlink type simple xlink href someHeading a link anchor ... with resources without editing those resources. XLink also supports richer information about link types and the roles of each resource in an arc. Support for XLink Within other specifications SVG ... 31 Corrected Errata 2008 07 02.htm 3.5 title Extensible Business Reporting Language XBRL 2.1 XLink .... As of 2009, XBRL is probably the most extensive use of XLink in production systems. METS The METS ... referencing. In particular, GML uses xlink href to support a graph model for geospatial information ... in XML documents. ref citation url https developer.mozilla.org en XLink title XLink MDC publisher Mozilla ref Only the code xlink href code , code xlink show code , code xlink target code and code xlink title code attributes are supported. ref citation url https developer.mozilla.org en ... http www.w3.org TR xlink11 W3C Recommendation http www.w3.org TR xlink W3C Recommendation version 1.0 http www.xml.com pub a 2002 03 13 xlink.html XLink Who Cares? http www.w3.org XML 2000 09 LinkingImplementations.html ... more details
replacements such as DD WRT or SlugOS . Features Xlink Kai supports Xbox, Xbox 360, PlayStation ... XLink website. ref http n4g.com news 554911 hackers remove the xbox 360s 30ms ping limit for system link. ref Xbox Media Center and XLink Kai Deleted image removed File MC360 Blackbolt XLink Kai.jpg thumb right MC360 skin for XLink Kai on Xbox XBMC Xbox Media Center XBMC for Microsoft s Xbox console has a control client for XLink Kai that allows control of the XLink Kai software program from the user s Xbox via XBMC GUI. MC360 is a skin for XBMC by Blackbolt that gives the XLink Kai ... for friends, arenas, etc. XLink Kai was removed from XBMC builds 14099 and later. To use ... of XBMC. References reflist External links http www.teamxlink.co.uk teamxlink.co.uk XLink Kai official website DEFAULTSORT Xlink Kai Category PlayStation 2 Category Nintendo Category Nintendo GameCube ... de XLink Kai es XLink Kai nl XLink Kai ja Xlink Kai sv XLink Kai ... more details
Unreferenced date October 2010 orphan date December 2009 XLINK originally was the eXterne Lokale Informatik Netz Karlsruhe the external connection of the computer science network of the universities in Karlsruhe, Germany . It was created in 1984, when it offered one of the first UUCP connections from Germany to the USA via UUNET , and from November 1989 it also offered Internet connectivity mainly to universities in the south of Germany. XLINK was one of the founding members of RIPE and of DENIC its autonomous system number autnum was AS517. It was transformed into part of a company in 1993, and as such, competed with the UniDO ISP incorporated as EUnet Germany for the title of first commercial Internet service provider in Germany. It was bought by Qwest in 1999 and contributed to and renamed to KPNQwest Germany in May 2000, which went bankrupt in the Internet bubble crash of 2002. Remnants exist in KPN Eurorings. References Reflist External links http www.xlink.de History of XLINK in German Category Internet in Germany Category Internet service providers ... more details
In computing , Resource Directory Description Language RDDL is an extension of XHTML Basic 1.0. An RDDL document, called a Resource Directory, provides a package of information about some target. The targets which RDDL was designed to describe are XML namespace s. The specification for RDDL has no official standing and has not been considered nor approved by any organization e.g., W3C . RDDL is designed to allow both human readers and software robots to find any sort of resource associated with a particular namespace. Instead of putting one thing at the end of a namespace Uniform Resource Identifier URI , RDDL puts a document there that lists all the machine processable documents that might be available, including, but not limited to Document Type Definition s DTD XML schema s in a variety of languages including RELAX , Schematron , W3C XML Schema , TREX , and others Cascading Style Sheets , XSLT , and other style sheet specifications Specification documents rddl resource An RDDL document identifies each related resource by a resource element in the http www.rddl.org namespace, which is customarily mapped to the rddl prefix. This element is a simple XLink that is, it has an code xlink type code attribute with the value simple and its code xlink href code attribute points to the related resource. Furthermore, the code xlink role code attribute identifies the nature of the related resource and the optional code xlink arcrole code attribute identifies the purpose of the related resource. An optional code xlink title code attribute can provide a brief description of the purpose of the link. External links http www.rddl.org RDDL home page http xml.coverpages.org rddl.html Cover Pages Resource Directory Description Language RDDL http www.oreillynet.com pub a oreilly xml news xmlnut2 0201.html What does a namespace URI locate? compu lang stub Category HTML ... more details
Schema W3C XML Schema , XLink , XPath , and XML namespace Namespaces . One use of XBRL is to define .... XBRL uses XML Schema W3C XML Schema , XLink , and XPointer standards. XBRL Instance The XBRL instance ... nature must use a unit from the ISO 4217 namespace. Footnotes use XLink to associate one or more facts ... 2003 linkbase xmlns xlink http www.w3.org 1999 xlink xbrll schemaRef xbrll href http www.org.com xbrl taxonomy xlink type simple ifrs gp OtherOperatingIncomeTotalFinancialInstitutions contextRef ... schema document file . Linkbases are XML documents file which follow the XLink specification ... below. source lang xml label xlink type resource xlink role http www.xbrl.org 2003 role label xlink label ifrs AssetsTotal lbl xml lang en Assets, Total label label xlink type resource xlink role http www.xbrl.org 2003 role label xlink label ifrs AssetsTotal lbl xml lang de Verm genswerte, Gesamt label label xlink type resource xlink role http www.xbrl.org 2003 role label xlink label ifrs AssetsTotal ... an element will be used. source lang xml label xlink type resource xlink role http www.xbrl.org 2003 role label xlink label ifrs AssetsTotal lbl xml lang en Property, Plant and Equipment, Net label label xlink type resource xlink role http www.xbrl.org 2003 role periodStartLabel xlink label ifrs AssetsTotal lbl xml lang en Property, Plant and Equipment, Net, Beginning Balance label label xlink type resource xlink role http www.xbrl.org 2003 role periodEndLabel xlink label ifrs AssetsTotal lbl ... be provided for each element. source lang xml reference xlink type resource xlink role http www.xbrl.org 2003 role presentationRef xlink label CashFlowsFromUsedInOperationsTotal ref ref Name IAS ref Name ref Number 7 ref Number ref Paragraph 14 ref Paragraph reference reference xlink type resource xlink role http www.xbrl.org 2003 role measurementRef xlink label CashFlowsFromUsedInOperationsTotal .... source lang xml calculationArc xlink type arc xlink arcrole http www.xbrl.org 2003 arcrole summation ... more details
In computer science , particularly in human computer interaction , presentation semantics specify how a particular piece of a formal language is represented in a distinguished manner accessible to human senses , usually human vision. For example, saying that code nowiki bold ... bold nowiki code must render the text between these constructs using some bold typeface is a specification of presentation semantics for that syntax . An example of interactive presentation semantics is defining the expect behavior of a Hyperlink hypertext link on a suitable syntax. Many markup languages like HTML , CSS , DSSSL , XSL FO or troff have presentation semantics, but others like XML , XLink and XPath do not. ref H. P. Alesso, Craig Forsythe Smith, Developing Semantic Web services , A K Peters, Ltd., 2005, ISBN 1568812124, p. 62 and p. 100 ref ref G. Ken Holman, Definitive XSL FO , Prentice Hall PTR, 2003, ISBN 0131403745, p. 13 ref ref Erik Wilde, David Lowe, Xpath, XLink, XPointer, and XML a practical guide to Web hyperlinking and transclusion , Addison Wesley, 2003, ISBN 0201703440, p. 201 ref Character encoding standards like Unicode also have presentation semantics. ref http publib.boulder.ibm.com infocenter printer v1r1 index.jsp?topic com.ibm.printers.infoprintfonts com.ibm.printers.usingopentypefontsinanafpsystem g3a02mst18.htm ref One of the main goals of style sheet language s like CSS is to separate the syntax used to define structured data from the syntax endowed with presentation semantics that is used to render the data in various ways. References reflist compu sci stub Category Semantics Category Human computer interaction Category Programming language topics ... more details
Image Wien Fillgraderstiege Frontal.jpg thumb Fillgraderstiege The Fillgraderstiege is a staircase in the sixth district of Vienna , Mariahilf . It was built from 1905 to 1907 and designed by Max Hegele, a student of Victor Luntz and Carl Hasenauer , in an Art Nouveau style to connect the two streets, Fillgradergasse and Theobaldgasse. The stairs were blocked off in 1981, having been worn down for almost 80 years, and were then repaired between 1982 and 1984, in the process of which a caf and art gallery were added in a previously unused inner room behind the stairs, both of which opened on the 1 August 1985. The Fillgraderstiege staircase was named the fourth most beautiful steps in Europe in a 2004 poll of European art professors . ref de icon cite web url https www.wien.gv.at vtx vtx rk xlink?SEITE 020040830001 title Die sch nsten Stiegen von Wien und Europa publisher Vienna City of Vienna date 2004 08 30 ref References Reflist External links de icon http www.gumpendorferstrasse.at indexuser.php?id 7 Das Fillgrader The bar on the steps coord 48 12 00 N 16 21 31 E region AT 9 type landmark display title Staircases of Mariahilf Category Buildings and structures completed in 1907 Category Buildings and structures in Vienna Category Mariahilf Architecture stub Austria struct stub Vienna geo stub de Fillgraderstiege no Fillgraderstiege ... more details
Thea Leitner born June, 1921 in Vienna is an Austria n author and journalist. She has written numerous books for young people and was decorated, in May, 2003 for service to Vienna with the Silbernes Ehrenzeichen f r Verdienste um das Land Wien the Silver Order of Merit for Service to Vienna . She was the wife of German commentator and science popularizer Sebastian Leitner with whom she lived in Vienna until his death in 1989. Bibliography K rner aus der N he . 1951 Das Bilderbuch vom Bauernhof . ISBN 3 219 10315 4 Habsburgs verkaufte T chter . 1987, ISBN 3800032481, ISBN 978 3800032488 Schicksale im Hause Habsburg . 2003, ISBN 3492239803 Habsburgs Goldene Br ute. Durch Mitgift zur Macht . 2003, ISBN 3492235255 H hnerstall und Nobelball. Leben in Krieg und Frieden 1938 1955 . 2003, ISBN 3800039273 autobiographical External links http www.ceiberweiber.at 2004 leitner.htm Lebensgeschichte in German http www.wien.gv.at vtx vtx rk xlink?SEITE 020030507008 Magistrat Wien Ehrung in German PND 123664446 Persondata NAME Leitner, Thea ALTERNATIVE NAMES SHORT DESCRIPTION Austrian writer DATE OF BIRTH June, 1921 PLACE OF BIRTH Vienna , Austria DATE OF DEATH PLACE OF DEATH DEFAULTSORT Leitner, Thea Category Austrian writers Category People from Vienna Category 1921 births Category Living people de Thea Leitner pl Thea Leitner ru , ... more details
context date May 2010 A fat link also known as a one to many link, an extended link ref XML Linking Language XLink Version 1.0 accessed 2010 1 27 http www.w3.org TR xlink extended link ref or a multi tailed link ref HTML, Web Browsers, and Other Paraphernalia accessed 2011 08 15 http www.duke.edu mshumate fiction htt tools.html ref is a hyperlink which leads to multiple endpoints the link is a multivalued function . blockquote The hyperlinks that are attached to the same design object can be grouped into a fat link for representational purposes, and the activation of a fat link gives a menu of the links contained in it cf. hyperlink history list , from which individual links can then be activated. ref Harri Oinas Kukkonen, Embedding Hypermedia into Information Systems, hicss, p. 187, 30th Hawaii International Conference on System Sciences HICSS Volume 6 Digital Documents, 1997. ref blockquote The concept is also covered in Gr nb k and Trigg s extended Dexter model ref Gr nb k, K. and Trigg, R. H. 1996. Toward a Dexter based model for open hypermedia unifying embedded references and link objects. In Proceedings of the Seventh ACM Conference on Hypertext Bethesda, Maryland, United States, March 16 20, 1996 . HYPERTEXT 96. ACM Press, New York, NY, 149 160. ref , which cites the Instructional Design Environment ref Jordan, D. S., Russell, D. M., Jensen, A. S., and Rogers, R. A. 1989. Facilitating the development of representations in hypertext with IDE. In Proceedings of the Second Annual ACM Conference on Hypertext Pittsburgh, Pennsylvania, United States . HYPERTEXT 89. ACM Press, New York, NY, 93 104. ref . The concept pre dates the World Wide Web ref T. Berners Lee et al., World Wide Web The Information Universe , Electronic Networking Research, Applications and Policy , 1 2 , 1992. ref . However, there have been calls for fat links to be implemented on the web e.g. Jakob Nielsen usability consultant Jakob Nielsen in his Alertbox for January 3, 2005 ref Nielsen, Jako ... more details
Plain Old XML POX is a term used to describe basic XML , sometimes mixed in with other, blendable specifications like XML namespace XML Namespaces , Dublin Core , XInclude and XLink . People typically use the term as a contrast with complicated, multilayered XML specifications like those for web service s or Resource Description Framework RDF . The term may have been derived from or inspired by the expression plain old telephone service a.k.a. POTS and, similarly Plain Old Java Object . An interesting question is how POX relates to XML Schema W3C XML Schema . On the one hand, POX is completely compatible with XML Schema. However, many POX users eschew XML Schema to avoid the poor or inconsistent quality of XML Schema to Java tools. Fact date January 2009 POX is complementary to Representational State Transfer REST REST refers to a communication pattern, while POX refers to an information format style. The primary competitors to POX are more strictly defined XML based information formats such as Resource Description Framework RDF and SOAP protocol SOAP section 5 encoding , as well as general non XML information formats such as JSON and Comma separated values CSV . External links http msdn.microsoft.com en us library aa395208.aspx REST and POX article from the Microsoft Developer Network http microformats.org wiki plain old xml considered harmful Plain Old XML Considered Harmful from Microformats.org http static.springsource.org spring ws sites 1.5 apidocs org springframework ws pox package summary.html Support for POX in the Java Spring Framework http sourceforge.net projects plainxml PlainXML on SourceForge.net Category XML compu lang stub es Plain Old XML POX ... more details
right valign bottom Image Xlink dominant mother.jpg thumb 175px align left valign bottom Image X ... Image Xlink dominant mother.jpg gallery br clear all When the father alone is the carrier of a defective ... more details
Context date November 2009 HyTime Hypermedia Time based Structuring Language is a markup language that is an application of SGML . HyTime defines a set of hypertext oriented element types that, in effect, supplement SGML and allow SGML document authors to build hypertext and multimedia presentations in a standardized way. HyTime is an international standard published by the International Organization for Standardization ISO and International Electrotechnical Commission IEC . The first edition was published in 1992, and the second edition was published in 1997. Legacy Some of the concepts formalized in HyTime were later incorporated into HTML and XML HTML is an application of SGML for hypertext document presentations, that assigns specific semantics and processing expectations to a fixed set of element types. XML defines a simplified subset of SGML that focuses on providing an open vocabulary of element types for data modeling and establishes precise expectations for how the markup computing marked up data is read and subsequently fed to another software application for further processing, but does not assign semantics to the element types or establish expectations for how the data is processed. XLink was intended as a simplified version of HyTime for use in the XML world, but has not seen much adoption. Work on applying HyTime to back of book indexes eventually led to the development of Topic Maps , which eventually became far more successful in its own right than HyTime ever was. Standard The HyTime standard itself is ISO IEC 10744, first published in 1992 and available from the International Organization for Standardization . It was developed by ISO IEC JTC1 SC34 ISO IEC Joint Technical Committee 1, Subcommittee 34 Document description and processing languages . ref cite web url http www.iso.org iso iso technical committee.html?commid 45374 title JTC 1 SC 34 Document description and processing languages author ISO publisher ISO accessdate 2009 12 25 ref ref cite w ... more details
Technical date September 2009 Nested Context Language NCL is a declarative authoring language for hypermedia documents. NCL is an XML application language, which provides several facilities for authoring a complete hypermedia document with synchronization relationships among its components. Among its main facilities, it treats hypermedia relations as first class entities through the definition of hypermedia connectors, and it can specify arbitrary semantics for a hypermedia composition using the concept of composite templates. Following others XML standards, NCL is specified by a modular approach. NCL modules can be added to standard web languages, such as XLink and Synchronized Multimedia Integration Language SMIL . NCL was initially designed for the Web environment, but currently it is included as the declarative language of the Japanese Brazilian ISDB Tb International Standard for Digital Broadcasting terrestrial DTV digital TV middleware named Ginga SBTVD Middleware Ginga . It is also the first standardized technology of the ITU T multimedia application framework series of specifications for IPTV services. NCL Historical Evolution NCL 3.0 Profiles Full Profile NCL 3.0 Full Profile includes all NCL Modules. Enhanced Digital TV profile EDTV NCL 3.0 Enhanced DTV profile includes the Structure, Layout, Media, Context, MediaContentAnchor, CompositeNodeInterface, PropertyAnchor, SwitchInterface, Descriptor, Linking, CausalConnectorFunctionality, ConnectorBase, TestRule, TestRuleUse, ContentControl, DescriptorControl, Timing, Import, EntityReuse, ExtendedEntityReuse, KeyNavigation, Animation, TransitionBase, Transition and Metainformation modules of NCL 3.0. NCL Basic Digital TV profile BDTV Includes almost all Enhanced Digital TV profiles but it doesn t include Animation , TransitionBase and Transition modules. NCL 3.0 Modules NCL is partitioned in functional areas. Each functional area groups a set of related modules. NCL 3.0 functional areas and modules are Structur ... more details
Image Gcbba.jpg thumb The GameCube BBA, attached to a GameCube The Nintendo GameCube Broadband Adapter and Modem Adapter are a network card network adapter and 56k Dial up access dial up modem , respectively, for the Nintendo GameCube . They were produced by Conexant and made in the Philippines . The adapters fit flush into Serial Port 1 on the underside of the GameCube and add a 8P8C RJ 45 or 6P4C Registered jack RJ 11 port to the side of the console. ref Cite book url http www.nintendo.com consumer downloads broadband english.pdf title Broadband Adapter Instruction Booklet publisher Nintendo location USA year 2002 format PDF accessdate 2010 08 15 ref Online and LAN play The adapters enable online play for four titles Phantasy Star Online Episode I & II , Phantasy Star Online Episode I & II Plus , and Phantasy Star Online Episode III C.A.R.D. Revolution from Sega , and Homeland video game Homeland from Chunsoft , which was only released in Japan. The broadband adapter allows Local area network LAN play with Mario Kart Double Dash , Kirby Air Ride , and 1080 Avalanche . Warp Pipe and XLink Kai have created unofficial tunneling software that allows these games to be played over the Internet. Possibilities for running unsigned code Soon after PSO I & II was released for the GameCube, it was discovered that a Personal computer PC could be made to simulate the conditions of the server that the game would connect to. This information started as a method of Tunneling protocol tunneling the online service. When simulating this server, unsigned code can be streamed back to the GameCube, allowing homebrew video games homebrew , or information could be streamed back, allowing one to play copied games. This was also implemented to allow online gameplay in games for which it is not intended. Early dumps of GameCube games were created using this technique. From there, methods of running the games off of a computer through a GameCube were created. Nintendo and Sega responded by r ... more details
Infobox Disease Name Bazex Dupre Christol syndrome Image Caption DiseasesDB 34543 ICD10 ICD9 ICDO OMIM 301845 MedlinePlus eMedicineSubj eMedicineTopic MeshID Bazex Dupre Christol syndrome also known as Bazex syndrome, ref name Bolognia and Follicular atrophoderma and basal cell carcinomas ref name Bolognia cite book author Rapini, Ronald P. Bolognia, Jean L. Jorizzo, Joseph L. title Dermatology 2 Volume Set publisher Mosby location St. Louis year 2007 pages isbn 1 4160 2999 0 oclc doi accessdate ref is a very rare condition inherited in an X linked dominant fashion. Physical findings typically include follicular atrophoderma , multiple basal cell carcinoma s, hypotrichosis and hypohidrosis . ref Bolognia,J 2008 Dermatology , Mosby, ISBN 9781416029991. ref This condition should not be confused with the unrelated condition Acrokeratosis paraneoplastica of Bazex , which may also be referred to Bazex syndrome. Genetics Double image right Xlink dominant mother.jpg 185 X link dominant father.jpg 185 X linked dominant inheritance works differently depending upon whether the mother left image or father right image is the carrier of a gene that causes a disease or disorder BCDS is inherited in an X linked dominant manner. This means the defective gene responsible for the disorder is located on the X chromosome, and only one copy of the defective gene is sufficient to cause the disorder when inherited from a parent who has the disorder. Males are normally Zygosity Hemizygous hemizygous for the X chromosome, having only one copy. As a result, X linked dominant disorders usually show higher expressivity in males than females. As the X chromosome is one of the sex chromosome s the other being the Y chromosome , X linked inheritance is determined by the gender of the parent carrying a specific gene and can often seem complex. This is because, typically, female s have two copies of the X chromosome, while male s have only one copy. The difference between Dominance genetics Dominan ... more details
Merge Typed link discuss Talk Typed link Merge Typed link and Link relation ? date October 2011 HTML A link relation is a descriptive attribute attached to a hyperlink in order to define the type of the link, or the relationship between the source and destination resources. The attribute can be used by automated systems, or can be presented to a user in a different way. In HTML these are designated with the tt rel tt attribute on tt link tt , tt a tt or tt area tt elements. Example uses include the standard way of referencing Cascading Style Sheets CSS tt link rel stylesheet href example.css tt , which indicates that the external resource linked to with the tt href tt attribute is a stylesheet, so a web browser will generally fetch this file to render the page. Another example is tt rel favicon tt for the popular favicon icon. ref Cite web url http www.w3.org 2005 10 profile publisher World Wide Web Consortium accessdate 23 February 2011 title Web site meta data profile favicon, year 2005 month October first Karl last Dubost ref ref Cite web url http www.w3.org 2005 10 howto favicon title How to Add a Favicon to your Site last Dubost first Karl date 24 October 2005 publisher World Wide Web Consortium accessdate 25 February 2011 ref Link relations are used in some microformat s e.g. tt rel tag tt for Tag metadata tagging , in XHTML Friends Network XFN , and in the Atom standard Atom standard , in XLink , as well as in HTML. Standardized link relations are one of the foundations of HATEOAS as they allow the user agent to understand the meaning of the available state transitions in a Representational State Transfer REST system. The Internet Engineering Task Force IETF has a registry of standardized link relations, ref name link relations registry http www.iana.org assignments link relations link relations.xhtml IANA link relations registry ref and a procedure for extending it defined in RFC 5988. HTML 5 also defines valid link relations. ref name HTML 5 link relations ... more details
style width 12 Prince XML style text align left XLink ref group spec citation url http www.w3.org TR xlink11 title XML Linking Language XLink Version 1.1 publisher W3C ref yes 5.0 partial tag ref ... . ref group g citation url https developer.mozilla.org en XLink title XLink MDC publisher Mozilla ... title Bug 10556 Support XLink in any XML document publisher WebKit ref no partial partial tag ref ... more details
Infobox disease Name X linked hypophosphatemia Image Caption DiseasesDB 6513 ICD10 ICD10 E 83 3 e 70 ICD9 ICD9 275.3 ICDO OMIM 307800 MedlinePlus eMedicineSubj ped eMedicineTopic 1128 MeshName MeshNumber MeshID D053098 X linked hypophosphatemia XLH , also called X linked dominant hypophosphatemic rickets , X linked vitamin d resistant rickets or hypophosphatemic vitamin d resistant rickets HPDR , ref name omim OMIM 307800 ref is an X linked dominant form of rickets or osteomalacia that differs from most cases of rickets in that ingestion of vitamin D is relatively ineffective. It can cause bone deformity including short stature and genu varum bow leggedness . It is associated with a mutation in the Phosphate regulating endopeptidase gene PHEX gene sequence Xp.22 and subsequent inactivity of the PHEX protein. ref name xlhxd The prevalence of the disease is 1 20000. ref cite journal author Carpenter TO title New perspectives on the biology and treatment of X linked hypophosphatemic rickets journal Pediatr. Clin. North Am. volume 44 issue 2 pages 443 466 year 1997 month Apr pmid 9130929 doi 10.1016 S0031 3955 05 70485 5 url ref The leg deformity can be treated with Ilizarov frame s and CHAOS surgery . Cause and Genetics Double image right Xlink dominant mother.jpg 185 X link dominant father.jpg 185 X linked dominant inheritance works differently depending upon whether the mother left image or father right image is the carrier of a gene that causes a disease or disorder XLH is associated with a mutation in the Phosphate regulating endopeptidase gene PHEX gene sequence, located on the human X chromosome at location Xp22.2 p22.1. ref name omim ref name xlhxd ref OMIM 300550 ref The mutation results in altered or missing activity of the PHEX protein, which inactivates hormone like substances phosphatonins that promote phosphate excretion. The resulting excess excretion of phosphate impairs bone mineralization. Biochemically, XLH is recognized by hypophosphatemia and inappr ... more details
unreferenced date September 2011 DDL D escription D efinition L anguage is part of the MPEG 7 standard. It gives an important set of tools for the users to create their own Description Scheme s DSs and Descriptors Ds . DDL defines the syntax rules to define, combine, extend and modify Description Schemes and Descriptors. Introduction DDL is not a modeling language, such as the Unified Modeling Language Unified Modeling Language UML , but a schematic language to represent the audiovisual data results, which must conform to the descriptors, the description schemes and the MPEG 7 descriptions. MPEG 7 DDL Must Be able to express relationships of elements within a DS or between two DS, whether they are structural, spatial, temporal, conceptual or hierarchical. Give a rich set of unions and references between one or more descriptions and the data they describe. Be application and platform independent. Be able to specify the descriptors data type, whether they are primary integers, text, time, ... or derived enumerated, ... History In 1999, the team in charge of MPEG 7 DDL was comparing and evaluating proposals in the MPEG 7 AHG Test And Evaluation Meeting held in Lancaster. The main agreement was that DDL had to use the XML syntax, support object oriented semantics, as well as being able to validate structural, relational and data typing constraints. Although no proposal satisfied the requirements the Distributed Systems Technology Centre DSTC proposal was used as a starting point, extending it with the additions of ideas and components from other proposals and contributors. Moreover, the strategy was to keep tracking and influencing the W3C community, specially the XML Schema W3C XML Schema , XLink , XPath and XPointer working groups. At the 51st MPEG meeting, the adoption of the XML Schema syntax with specific MPEG 7 extensions was decided. Requirements As defined in the MPEG 7 requirements document Compositional capabilities DDL shall allow new DSs and Ds to be created ... more details
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